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Original Article
Three Cases of Single Ventricle with Asplenia.
Bong Shin Lee, Yoo Ho Kim, Byoung Hai Ahn, Young Hee Yoo, Hyun Suk Lee, Jeong Rye Kim, Wook Younm
Clin Exp Pediatr. 1988;31(10):1358-1365.   Published online October 31, 1988
Congenital asplenia syndrome is associated with malposition and malformation of other organ system such as congenital heart disease, patial or complete situs inversus, symmetric lobulation of the liver and the lung. This is a rare syndrome but has been reported in increaseing frequency in recent years. We experienced three cases of this single ventricle with asplenia. One is confirmed by autopsy and the others are...
Case Report
One Case of a 18-Year-Old Boy with Domplete D-Transposition of the Great Arteries.
Tae Kyoung Kim, Bong Shin Lee, Byoung Hai Ahn, Young Hi Yoo, Hyun Suk Lee, Wook Youm
Clin Exp Pediatr. 1987;30(5):569-576.   Published online May 31, 1987
Without the appropriate treatment, infants bom with transposition of the great arteries rarely survive the first year of life. But modern aggressive palliative and corrective surgical interventions can provide such infants with considerable hope for aldolescent and adult life. In this report, we present one case of a 18-year-old boy having complete D-transposition of the great arteries with atrial septal defect (S.D.D), who was...
Original Article
Congenital adrenal Hyperplasia.
Byoung Hai Ahn, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1986;29(6):604-612.   Published online June 30, 1986
Clinical data of twenty-eight children with congenital adrenal hyperplasia who were admitted to the Seoul National University Hospital from June 1979 to July 1984 were analyzed retrospectively. Male to female ratio was 1 : 1.3. The average age at diagnosis was 3.2 years, 1.3 months for eleven salt-losers and all were 3 months or younger, 4.6 years for seventeen nonsaltlosers....
Case Report
Three Cases of Familial Glucocorticoid Deficiency.
Soo Heum Lim, Young Wun Kim, Byoung Hai Ahn, Hyung Ro Moon
Clin Exp Pediatr. 1986;29(5):549-552.   Published online May 31, 1986
Familial glucocorticoid defiency is a form of chronic adrenal insufficiency which is characterized by isolated deficiency of glucocorticoid and elevated levels of corticotropin in association with normal aldosterone production. It is thought to be degenerative process of adrenal cortex, with autosomal recessive or X-linked recessive pattern of inheritance. Skin hyperpigmentation and hypoglycemic symptom are characteristic and salt-losing symptom doesn’t develop....
Three Cases of Nephrogenic Diabetes Insipitus.
Hey Sun Lee, Byoung Hai Ahn, Jong Jin Seo, Hyung Ro Moon
Clin Exp Pediatr. 1984;27(9):912-917.   Published online September 30, 1984
From July 1981 to Feb. 1983, we experienced three cases of nephrogenic diabetes insipidus in which the initial diagnostic clues were repeated episodes of unexplained fever in infancy and which were confirmed by water deprivation and pitressin tests and clinical responses to administration of hydrochlorthiazide. So we report this with some review of literatures.
A Case of Pierre Robin Syndrome.
Hyun Hwa Kim, Hae Sook Cha, Byoung Hai Ahn, Young Hee You, Hyun Sook Lee
Clin Exp Pediatr. 1984;27(5):488-492.   Published online May 31, 1984
A case ef Pierre Robin Syndrome in a male baby who was born at the Korea Veterans Hospital was presented. After birth, dyspnea and feeding difficulty were developed. Physical examination revealed micrognathia, glossoptosis and cleft plate. Chromosomal analysis was normal pattern. This finding was compatible with Pierre Robin Syndrome. A brief review of literature was presented.
Moyamoya Disease with Intraventricular Hemorrhage in a Child.
Byoung Hai Ahn, Chung Il Noh, Yong Seung Hwang, Young Soo Yoon
Clin Exp Pediatr. 1983;26(12):1247-1253.   Published online December 31, 1983
A 9-year-old female patient with evidence of intraventricular hemorrhage by computed tomography was subsequently proven to have moyamoya disease by cerebral angiography. Subarachnoid hemorrhage is the most common initial manifestation of moyamoya disease in the adult. However, such presentation seldom occurs in childhood moyamoya disease, and intraventricular hemorrhage has been quite rare in children. The rarity of this manifestation of moyamoya disease and its cause...
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